Clinical Trials - RARE

NCT IDTitleStatusPhasesStart DateCompletion DatePrimary Completion Date
NCT07157254A Safety and Efficacy Study of GTX-102 in Subjects With Deletion- or Nondeletion-type Angelman Syndrome (AS)RECRUITINGPHASE22025-112030-012030-01
NCT06617429Phase 3 Efficacy and Safety Study of GTX-102 in Pediatric Subjects With Angelman Syndrome (AS)ACTIVE_NOT_RECRUITINGPHASE32024-12-032027-112026-07
NCT06636071Setrusumab in Pediatric Japanese Subjects With Osteogenesis ImperfectaACTIVE_NOT_RECRUITINGPHASE32024-10-252028-012027-01
NCT06415344Long-term Extension of GTX-102 in Angelman SyndromeENROLLING_BY_INVITATIONPHASE32024-07-312029-022029-02
NCT05768854Setrusumab vs Bisphosphonates in Pediatric Subjects With Osteogenesis ImperfectaACTIVE_NOT_RECRUITINGPHASE32023-06-142027-042026-03
NCT05933200A Study to Determine the Effect of Triheptanoin Compared With Even-Chain MCT on MCEs in Pediatric Patients With LC-FAODACTIVE_NOT_RECRUITINGPHASE32023-02-282027-082027-08
NCT05345171Clinical Study of DTX301 AAV-Mediated Gene Transfer for Ornithine Transcarbamylase (OTC) DeficiencyACTIVE_NOT_RECRUITINGPHASE32022-10-182031-032025-02-19
NCT05312697Long-term Extension Study of Setrusumab in Adults With Type I, III, or IV Osteogenesis ImperfectaTERMINATEDPHASE22022-04-282022-07-072022-07-07
NCT05125809Setrusumab vs Placebo for Osteogenesis ImperfectaACTIVE_NOT_RECRUITINGPHASE2, PHASE32022-02-212027-042026-03
NCT05139316A Study of Adeno-Associated Virus Serotype 8-Mediated Gene Transfer of Glucose-6-Phosphatase in Patients With Glycogen Storage Disease Type Ia (GSDIa)ACTIVE_NOT_RECRUITINGPHASE32021-11-082026-022024-02-20
NCT04990388Safety, Tolerability, and Pharmacokinetics of UX053 in Patients With Glycogen Storage Disease Type III (GSD III)TERMINATEDPHASE1, PHASE22021-10-182023-03-202023-03-20
NCT04884815A Phase 1/2/3 Study of UX701 Gene Therapy in Adults With Wilson DiseaseACTIVE_NOT_RECRUITINGPHASE1, PHASE22021-09-272034-032029-03
NCT04360265Follow-up Study of AAV-Mediated Gene Transfer (UX111; Previously Known as ABO-102) for MPS Type IIIAENROLLING_BY_INVITATIONPHASE32020-09-282027-082027-08
NCT04259281A Study of the Safety and Tolerability of GTX-102 in Children with Angelman SyndromeCOMPLETEDPHASE1, PHASE22020-02-242025-01-082025-01-08
NCT04088734Gene Transfer Study of ABO-102 in Patients With Middle and Advanced Phases of MPS IIIA DiseaseTERMINATEDPHASE1, PHASE22019-09-182022-03-102022-03-10
NCT03517085Safety and Dose-Finding Study of DTX401 (AAV8G6PC) in Adults With Glycogen Storage Disease Type Ia (GSDIa)COMPLETEDPHASE1, PHASE22018-05-182021-11-022021-11-02
NCT03216486An Exploratory Study of BPS804 Treatment in Adult Patients With Type I, III or IV Osteogenesis ImperfectaWITHDRAWNPHASE22017-10-312018-11-012018-11-01
NCT03118570A Study in Adult Patients With Type I, III or IV Osteogenesis Imperfecta Treated With BPS804COMPLETEDPHASE22017-09-112020-11-122019-10-01
NCT02991144Safety and Dose-Finding Study of DTX301 (scAAV8OTC) in Adults With Late-Onset Ornithine Transcarbamylase (OTC) DeficiencyCOMPLETEDPHASE1, PHASE22017-07-312021-12-162021-12-16
NCT02960217Crossover Study to Assess the Efficacy and Safety of UX007 in the Treatment of Movement Disorders Associated With Glucose Transporter Type 1 Deficiency Syndrome (Glut1 DS)TERMINATEDPHASE32017-04-192019-10-092019-10-09
NCT02736188Study to Evaluate the Safety and Efficacy of Aceneuramic Acid Extended-Release (Ace-ER) Tablets in Patients With Glucosamine (UDP-N-acetyl)-2-epimerase Myopathy (GNEM) or Hereditary Inclusion Body Myopathy (HIBM)TERMINATEDPHASE32016-05-022018-01-102018-01-10
NCT02731690A Study to Evaluate the Safety of Aceneuramic Acid Extended Release (Ace-ER; UX001) Tablets in Glucosamine (UDP-N-acetyl)-2-Epimerase (GNE) Myopathy (GNEM) (Also Known as Hereditary Inclusion Body Myopathy [HIBM]) Patients With Severe Ambulatory ImpairmentTERMINATEDPHASE22016-04-292018-01-102018-01-10
NCT02716246Phase I/II/III Gene Transfer Clinical Trial of scAAV9.U1a.hSGSHRECRUITINGPHASE2, PHASE32016-04-252027-072027-07
NCT02618915Safety and Dose Finding Study of DTX101 (AAVrh10FIX) in Adults With Moderate/Severe to Severe Hemophilia BTERMINATEDPHASE1, PHASE22015-12-162017-10-182017-10-18
NCT02432144A Study of UX003 Recombinant Human Beta-Glucuronidase (rhGUS) Enzyme Replacement Therapy in Subjects With Mucopolysaccharidosis Type 7, Sly Syndrome (MPS 7)COMPLETEDPHASE32015-11-102019-01-142019-01-14
NCT02599961Study to Assess the Long Term Safety and Efficacy of UX007 in Participants With Glucose Type 1 Deficiency Syndrome (Glut1 DS)TERMINATEDPHASE22015-09-102019-10-222019-10-22
NCT02418455Study of UX003 Recombinant Human Beta-Glucuronidase (rhGUS) Enzyme Replacement Treatment in Mucopolysaccharidosis Type 7, Sly Syndrome (MPS 7) Patients Less Than 5 Years of AgeCOMPLETEDPHASE22015-07-212019-03-262019-03-26
NCT02377921Phase 3 Randomized, Double-Blind, Placebo-Controlled Study to Evaluate Sialic Acid in Patients With Glucosamine (UDP-N-acetyl)-2-epimerase Myopathy (GNEM) or Hereditary Inclusion Body Myopathy (HIBM)COMPLETEDPHASE32015-05-202017-06-092017-06-09
NCT02214160Long-Chain Fatty Acid Oxidation Disorders (LC-FAOD) Extension Study for Subjects Previously Enrolled in Triheptanoin StudiesCOMPLETEDPHASE22014-12-092020-12-032020-12-03
NCT02230566A Phase 3 Study of UX003 Recombinant Human Betaglucuronidase (rhGUS) Enzyme Replacement Therapy in Patients With Mucopolysaccharidosis Type 7 (MPS 7)COMPLETEDPHASE32014-122016-052016-05
NCT01993186Phase 2 Study of Triheptanoin (UX007) for the Treatment of Glucose Transporter Type 1 Deficiency Syndrome (Glut1 DS)COMPLETEDPHASE22014-02-282017-09-202017-09-20
NCT01886378A Study of UX007 (Triheptanoin) in Participants With Long-Chain Fatty Acid Oxidation Disorders (LC-FAOD)COMPLETEDPHASE22014-02-062016-08-252016-08-25
NCT01856218An Open-Label Phase 1/2 Study to Assess the Safety, Efficacy and Dose of Study Drug UX003 Recombinant Human Beta-glucuronidase (rhGUS) Enzyme Replacement Therapy in Patients With Mucopolysaccharidosis Type 7 (MPS 7)COMPLETEDPHASE1, PHASE22013-112016-072016-07
NCT01806610Study of Safety and Tolerability of BPS804 in Patients With Late-stage Chronic Kidney DiseaseWITHDRAWNPHASE22013-082014-042014-04
NCT01830972An Open Label Phase 2 Extension Study of Higher Dose Sialic Acid-Extended Release (SA-ER) Tablets and Sialic Acid-Immediate Release (SA-IR) Capsules in Patients With Glucosamine (UDP-N-acetyl)-2-Epimerase (GNE) MyopathyCOMPLETEDPHASE22013-06-042017-02-142017-02-14
NCT01517880A Phase 2 Study to Evaluate the Dose and Pharmacodynamic Efficacy of Sialic Acid-Extended Release (SA-ER) Tablets in Patients With GNE Myopathy or Hereditary Inclusion Body MyopathyCOMPLETEDPHASE22012-052013-112013-11
NCT01406548Safety and Efficacy of Multiple Dosing Regimens of BPS804 in Post Menopausal Women With Low Bone Mineral DensityCOMPLETEDPHASE22011-072013-102013-10
NCT01406977Dose Escalation Study to Evaluate the Safety and Tolerability of Multiple Infusions of BPS804 in Adults With Hypophosphatasia (HPP)COMPLETEDPHASE22011-072012-092012-09
NCT01359319Safety and Pharmacokinetics of Sialic Acid Tables in Patients With Hereditary Inclusion Body Myopathy (HIBM)COMPLETEDPHASE12011-072012-052012-04
NCT01417091Safety, Pharmacokinetics and Pharmacodynamics of BPS804 in Osteogenesis ImperfectaCOMPLETEDPHASE22011-062012-122012-12